Arrhythmogenic right ventricular cardiomyopathy/dysplasia

Indik, Julia H and Marcus, Frank I (2003) Arrhythmogenic right ventricular cardiomyopathy/dysplasia. Indian Pacing and Electrophysiology Journal, 3 (3). pp. 148-156. ISSN 0972-6292

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Abstract

Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is characterized by the patchy replacement of myocardium by fatty or fibrofatty tissue. These changes lead to structural abnormalities including right ventricular enlargement and wall motion abnormalities that can be detected by echocardiography, angiography, and cine MRI. ARVC/D is a genetically heterogeneous disorder, since it has been linked to several chromosomal loci. Myocarditis may also be a contributing etiological factor. Patients are typically diagnosed during adolescence or young adulthood. Presenting symptoms are generally related to ventricular arrhythmias. Concern for the risk of sudden cardiac death may lead to the implantation of an intracardiac defibrillator. An ongoing multicenter international registry should further our understanding of this disease.

EPrint Type:Article
Uncontrolled Keywords:Arrhythmogenic Right Ventricular Cardiomyopathy, Dysplasia
Subjects:Cardiovascular Diseases > Heart Diseases > Arrhythmia > Tachycardia
Diagnosis > Diagnostic Techniques and Procedures > Diagnostic Techniques, Cardiovascular > Heart Function Tests > Electrocardiography
-Journal Repositories > Indian Pacing and Electrophysiology Journal
Cardiovascular Diseases > Heart Diseases
ID Code:268
Deposited By:Indian Pacing and Electrophysiology Journal
Deposited On:12 July 2005

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